Primary peritoneal cancer is an uncommon cancer of the abdominal lining that closely mirrors epithelial ovarian cancer in symptoms, spread, and treatment. Diagnosis relies on imaging, CA-125, and biopsy. Standard treatment is surgical cytoreduction followed by platinum-based chemotherapy. Maintenance therapies such as PARP inhibitors have become important for eligible patients, and options like HIPEC are under study. Prognosis varies by stage and residual disease; recurrence is common, so ongoing surveillance and genetic testing are recommended.
What primary peritoneal cancer is
Primary peritoneal carcinoma (PPC) is a cancer that arises from the lining of the abdomen (the peritoneum). It closely resembles epithelial ovarian cancer - especially high-grade serous carcinoma - in symptoms, pattern of spread, and biology. Because of this overlap, clinicians often manage PPC alongside ovarian and fallopian tube cancers.
How it's diagnosed
Symptoms are nonspecific: persistent abdominal bloating or swelling, early fullness while eating, abdominal pain or discomfort, and unintentional weight change (often from fluid, or ascites). Doctors use a combination of physical exam, imaging (usually CT), blood tests such as CA-125, and tissue biopsy - often obtained by laparoscopy - to confirm the diagnosis.
Genetic testing is important. Women with BRCA1/2 variants and other defects in homologous recombination are at increased risk for PPC, similar to ovarian cancer.
Standard treatment today
Treatment depends on how far the disease has spread and on the patient's fitness for surgery. The current backbone of care remains aggressive surgical cytoreduction (debulking) to remove as much tumor as possible, followed by platinum-based chemotherapy - most commonly carboplatin combined with paclitaxel.
Maintenance therapies have changed the landscape in the past decade. PARP inhibitors (for example, olaparib, niraparib, and rucaparib) are used as maintenance treatment after a response to platinum chemotherapy in many patients with ovarian-type cancers, and they are increasingly applied to PPC in eligible patients (for example, those with BRCA mutations or broader homologous recombination deficiency) .
Intraperitoneal approaches, including HIPEC (hyperthermic intraperitoneal chemotherapy) at the time of surgery, are used in selected centers and selected patients, but the benefit compared with standard approaches remains an area of active research 1.
Prognosis and follow-up
Prognosis varies widely and depends on stage at diagnosis, the amount of residual tumor after surgery, and tumor biology. PPC often responds to initial treatment but has a high risk of recurrence, so long-term surveillance with periodic exams, imaging, and CA-125 when helpful is standard.
Even after risk-reducing salpingo-oophorectomy (removal of ovaries and fallopian tubes), a small risk of developing primary peritoneal cancer remains - this is one reason genetic counseling and tailored follow-up matter.
Practical points
- See a gynecologic oncologist for diagnosis and treatment planning.
- Ask about genetic testing (BRCA and other genes) because results affect treatment options and family counseling.
- Discuss maintenance strategies and clinical trials, which can offer newer targeted options.
- Confirm current regulatory approvals and labeled indications for PARP inhibitors specifically mentioning primary peritoneal carcinoma (versus ovarian/fallopian tube cancers).
- Review recent randomized trials and guidelines on HIPEC use for primary peritoneal/ovarian-type cancers to clarify which patient groups, if any, benefit.
FAQs about Primary Peritoneal Cancer
How is primary peritoneal cancer different from ovarian cancer?
What are the main treatments for primary peritoneal cancer?
Should I have genetic testing if diagnosed with PPC?
Can primary peritoneal cancer come back after treatment?
Does removing the ovaries prevent PPC?
News about Primary Peritoneal Cancer
Mirvetuximab soravtansine approved to treat adult patients who have ovarian, fallopian tube or primary peritoneal cancer - GOV.UK [Visit Site | Read More]
Fertility-sparing surgery in primary peritoneal serous borderline tumor: a case report - Frontiers [Visit Site | Read More]
New Peritoneal Surface Malignancy Guidelines Aim to Improve Unity Among Oncologists - CancerNetwork [Visit Site | Read More]
Johnson & Johnson talc and cancer compensation claim - Consumer Voice [Visit Site | Read More]
FDA OKs Breakthrough Status for Sofetabart Mipitecan for Some Gynecologic Cancers - Cure Today [Visit Site | Read More]
Raludotatug Deruxtecan Granted Breakthrough Therapy Designation by U.S. FDA for Patients with CDH6 Expressing Platinum-Resistant Ovarian, Primary Peritoneal or Fallopian Tube Cancers Previously Treated with Bevacizumab - Business Wire [Visit Site | Read More]
PIPAC Reshapes Peritoneal Cancer Surgery Workflows and Outcomes: With Gregory J. Tiesi, MD, FACS, FSSO; Anthony Scholer, MD, FACS, FSSO; Benjamin Jon Golas, MD, FACS; and Eric Pletcher, MD - OncLive [Visit Site | Read More]
Survival rate for peritoneal cancer: Stages and screening - MedicalNewsToday [Visit Site | Read More]